Successful Repair of Unusual Complex of Aortic Atresia with Interrupted Aortic Arch: A Case Report

Authors

  • Zaher Faisal Zaher Department of Pediatric Cardiac Centre of Excellence, King Abdulaziz University, 22254 Jeddah, Saudi Arabia https://orcid.org/0000-0003-1736-9229
  • Ahmed Abdelrahman Elassal Department of Pediatric Cardiac Centre of Excellence, King Abdulaziz University, 22254 Jeddah, Saudi Arabia; Department of Surgery, Cardiac Surgery Unit, King Abdulaziz University, 22254 Jeddah, Saudi Arabia; Department of Cardiothoracic Surgery, Zagazig University, 7120001 Zagazig, Egypt https://orcid.org/0000-0002-2497-6978
  • Mazin Adel Fatani Department of Surgery, Cardiac Surgery Unit, King Abdulaziz University, 22254 Jeddah, Saudi Arabia
  • Feras Maher Fatani Department of Surgery, Cardiac Surgery Unit, King Abdulaziz University, 22254 Jeddah, Saudi Arabia https://orcid.org/0009-0000-7115-753X
  • Norah Bakheet Aljohani Department of Surgery, Cardiac Surgery Unit, King Abdulaziz University, 22254 Jeddah, Saudi Arabia https://orcid.org/0009-0006-1543-8349
  • Arwa Mohammed Alghamdi Department of Pediatric Cardiac Centre of Excellence, King Abdulaziz University, 22254 Jeddah, Saudi Arabia https://orcid.org/0009-0004-7139-3945
  • Osman Osama Al-Radi Department of Pediatric Cardiac Centre of Excellence, King Abdulaziz University, 22254 Jeddah, Saudi Arabia; Department of Surgery, Cardiac Surgery Unit, King Abdulaziz University, 22254 Jeddah, Saudi Arabia https://orcid.org/0000-0003-1261-1477

DOI:

https://doi.org/10.59958/hsf.8067

Keywords:

interrupted aortic arch, aortic atresia, aortopulmonary window, case report

Abstract

Interrupted aortic arch with aortic atresia is an unusual complex of congenital heart disease. Incompatibility for life is a potential risk unless there is blood flow in the ascending aorta supplying the coronary arteries from another existing malformations. We report a five days old case with interrupted aortic arch type B, aortic atresia, ventricular septal defect and an aortopulmonary window as a source of blood flow to the coronary arteries, ascending aorta and proximal aortic arch. A successful surgical correction with biventricular repair was performed. The significance of this is to expand the candidates for one stage total correction of congenital heart diseases in neonates, which spares patients multiple staged surgeries and spares health service providers the burden of multiple treatment strategies.

References

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Published

2025-02-18

How to Cite

Zaher, Z. F., Elassal, A. A., Fatani, M. A. ., Fatani, F. M. ., Aljohani, N. B. ., Alghamdi, A. M., & Al-Radi, O. O. (2025). Successful Repair of Unusual Complex of Aortic Atresia with Interrupted Aortic Arch: A Case Report. The Heart Surgery Forum, 28(2), E143-E147. https://doi.org/10.59958/hsf.8067

Issue

Vol. 28 No. 2 (2025)

Section

Case Report

Copyright (c) 2025 The Author(s)

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