Case Report: Nonarrhythmogenic Right Ventricular Dysplasia Presenting with Severe Right Ventricular Failure in an Adolescent


  • Mustafa Pac
  • Aysenur Pac
  • Tugcin Bora Polat
  • Sevket Balli
  • Nesrin Turhan
  • Dursun Aras
  • Mehmet Burhan Oflaz
  • Seref Kücüker



Right ventricular dysplasia is usually discovered by the presence of ventricular arrhythmia. As arrhythmia is an epiphenomenon, the first presentation of some cases can be primarily heart failure. We describe an adolescent girl who presented with progressive right heart failure and whose hallmark was fibrofatty replacement of ventricular muscle, especially of the right side, without ventricular arrhythmia. The patient was successfully treated by orthotopic heart transplantation.


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How to Cite

Pac, M., Pac, A., Polat, T. B., Balli, S., Turhan, N., Aras, D., Oflaz, M. B., & Kücüker, S. (2010). Case Report: Nonarrhythmogenic Right Ventricular Dysplasia Presenting with Severe Right Ventricular Failure in an Adolescent. The Heart Surgery Forum, 13(1), E21-E24.