Idiopathic Bradycardia in Unicuspid Unicommissural Aortic Valve Complicated with Infective Endocarditis and Aortic Root Abscess: A Case Report
DOI:
https://doi.org/10.1532/hsf.3671Keywords:
Unicuspid, unicommisural, infective endocarditis, heart block, Wheat procedureAbstract
Unicuspid aortic valves are among the rarest congenital malformations. They are classified as either acommissural or unicommissural, with the unicommissural being presented in early adulthood. Unicuspid valves share many similarities with bicuspid valves, namely increased rates of valve degeneration and calcification, making them prone to secondary aortic stenosis, regurgitation, or both. Among other similarities are the increased risk of aortic root dilatation, dissection, and left ventricular dilatation. We report our case of a 23-year-old male with unicuspid unicommissural aortic valve with aortic root and left ventricular dilatation. He successfully underwent Wheat procedure.
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