Surgical Treatment of Lutembacher Syndrome with a Huge Right Atrium: A Case Report

Authors

  • Maodong Yang Department of Cardiovascular Surgery, Yan’an Affiliated Hospital of Kunming Medical University, Kunming, China
  • Li Zhang Department of Cardiovascular Surgery, Yan’an Affiliated Hospital of Kunming Medical University, Kunming, China
  • Han Tang Department of Cardiovascular Surgery, Yan’an Affiliated Hospital of Kunming Medical University, Kunming, China
  • Linsong Liu Department of Cardiovascular Surgery, Yan’an Affiliated Hospital of Kunming Medical University, Kunming, China
  • Jian Wu Department of Cardiovascular Surgery, Yan’an Affiliated Hospital of Kunming Medical University, Kunming, China

DOI:

https://doi.org/10.1532/hsf.3641

Keywords:

Lutembacher’s syndrome, right atrium, atrial septal defect, mitral stenosis

Abstract

Background: Lutembacher’s syndrome (LS) is a rare cardiovascular anomaly that is defined as any combination of congenital or iatrogenic atrial septal defect (ASD) with congenital or acquired mitral stenosis (MS). The clinical features and hemodynamic effects of LS depend on the balance between ASD and MS.

Case Report: In this case report, we describe a rare case of LS with a huge right atrium in a 39-year-old male patient who was admitted to the hospital with worsening fatigue and breathlessness on exertion. Clinical examination revealed central cyanosis, raised jugular venous pressure bilaterally, clear breath sounds bilaterally with no dry and wet rales, hyperdynamic apex beat, and dull heart sounds. His vital signs on admission included blood pressure of 90/60 mmHg, irregular pulse of 76 beats/min, and oxygen saturation of 90.4%. Echocardiography revealed moderate to severe MS with ASD (ostium secundum). The patient’s condition deteriorated after initial medical management, and he underwent open heart surgery for mitral valve replacement, ASD repair, tricuspid annuloplasty, and right atrial volume reduction.

Conclusions: This case report describes the successful surgical management of this rare condition.

References

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Published

2021-04-07

How to Cite

Yang, M., Zhang, L., Tang, H., Liu, L., & Wu, J. (2021). Surgical Treatment of Lutembacher Syndrome with a Huge Right Atrium: A Case Report. The Heart Surgery Forum, 24(2), E359-E362. https://doi.org/10.1532/hsf.3641

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Section

Articles