Mediastinal Pheochromocytoma with Single Coronary Blood Supply: A Case Report


  • Andres Beiras-Fernandez
  • Peter Überfuhr
  • Ingo Kaczmarek
  • Konstantinou Nikolaou
  • Florian Weis
  • Theodor Rampp
  • Peter Lamm
  • Eckart Kreuzer
  • Bruno Reichart



Primary pheochromocytomas located outside the adrenal glands account for only 10% of all pheochromocytomas. Mediastinal pheochromocytomas are even rarer and usually represent a therapeutic challenge as they often infiltrate adjacent structures. We report the case of a large primary mediastinal pheochromocytoma in a 65-year-old patient presenting with a sudden angina-like chest pain and dyspnea. Thoracic multislice computed tomography showed an 8 x 5 x 6-cm retrocardiac mass causing compression of both atria and infiltrating the left superior pulmonary vein. The tumor was highly vascularized and presented a blood supply derived from the circumflex artery. The mass was successfully removed by open heart surgery, and the patient was discharged 10 days postoperatively.


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How to Cite

Beiras-Fernandez, A., Überfuhr, P., Kaczmarek, I., Nikolaou, K., Weis, F., Rampp, T., Lamm, P., Kreuzer, E., & Reichart, B. (2007). Mediastinal Pheochromocytoma with Single Coronary Blood Supply: A Case Report. The Heart Surgery Forum, 10(3), E196-E198.