Conventional Repair of an Intraoperatively Diagnosed Congenitally Corrected Transposition of the Great Arteries in an Adult

Authors

  • Muhammad Arza Putra, MD Thoracic and Cardiovascular Surgery Division, Department of Surgery, Faculty of Medicine, Universitas Indonesia, Cipto Mangunkusumo Hospital, Indonesia
  • Rubiana Sukardi, MD Integrated Cardiovascular Service, Cipto Mangunkusumo Hospital, Indonesia
  • Jonathan Grantomo, MD Thoracic and Cardiovascular Surgery Division, Department of Surgery, Faculty of Medicine, Universitas Indonesia, Cipto Mangunkusumo Hospital, Indonesia https://orcid.org/0000-0001-6104-6203
  • Jenni Pratita, MD Thoracic and Cardiovascular Surgery Division, Department of Surgery, Faculty of Medicine, Universitas Indonesia, Cipto Mangunkusumo Hospital, Indonesia https://orcid.org/0000-0002-1597-0435

DOI:

https://doi.org/10.1532/hsf.3249

Keywords:

congenitally corrected transposition of the great arteries, conventional repair, cardiac surgery

Abstract

Background: Congenitally corrected transposition of the great arteries (ccTGA) is a rare condition that accounts for just 1% of all congenital heart disease. Diagnosis of ccTGA often is missed in adulthood, despite imaging and cardiology consultation.

Case report: We present the case of an intraoperatively diagnosed ccTGA with severe tricuspid valve regurgitation and secundum atrial septal defect in a 54-year-old woman, who preoperatively was diagnosed with mitral valve regurgitation in atrioventricular and ventriculoarterial concordance heart. Intraoperatively, options considered were anatomical repair with atrial-arterial double switch operation after retraining the left ventricle or a conventional repair that focused on the associated defects without addressing the discordant connections. Considering our patient’s age and condition, we decided to carry on with the conventional repair to prevent further systemic right ventricle dysfunction that may lead to poor outcome and decreased survival. She was discharged one week after surgery and resumed her normal activity at 3-month follow up.

Conclusion: Although it rarely happens, CHD such as ccTGA in an adult must always be considered. Careful examination is essential. The treatment of ccTGA in an adult is challenging, with more limited options compared with pediatric patients. However, early management could still provide favorable outcomes.

References

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Published

2021-08-26

How to Cite

Putra, M. A., Sukardi, R., Grantomo, J., & Pratita, J. (2021). Conventional Repair of an Intraoperatively Diagnosed Congenitally Corrected Transposition of the Great Arteries in an Adult. The Heart Surgery Forum, 24(4), E769-E771. https://doi.org/10.1532/hsf.3249

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