Surgical management for an adult, female patient, with Ebstein Anomaly on Tricuspid Valve that has Subvalvular membrane with severe PS and multiple VSDs-A case report.

Authors

  • Saikat Das Gupta, MS Department of Cardiac Surgery, National Heart Foundation Hospital & Research Institute, Dhaka, Bangladesh
  • Mauin Uddin, MS, MRCSEd Department of Cardiothoracic Surgery, New Cross Hospital, Wolverhampton, UK
  • Siddhartha Shankar Howlader, MS Department of Cardiac Surgery, National Heart Foundation Hospital & Research Institute, Dhaka, Bangladesh
  • Prodip Kumar Biswas, MS Department of Cardiac Surgery, National Heart Foundation Hospital & Research Institute, Dhaka, Bangladesh
  • Mohammed Kabiruzzaman, MD Senior Consultant, Department of Cardiology, National Heart Foundation Hospital & Research Institute, Dhaka, Bangladesh
  • Mohammed Quamrul Islam Talukder, MD, FCPS, FCVS Senior Consultant, Department of Cardiac Surgery, National Heart Foundation Hospital & Research Institute, Dhaka, Bangladesh

DOI:

https://doi.org/10.1532/hsf.3233

Keywords:

Ebstein's anomaly (EA); Tricuspid Valve (TV) ; Ventricular Septal Defect (VSD); Pulmonary Stenosis (PS); Congenital heart defect , Right Ventricle (RV); Atrialized RV (aRV); Major Aortopulmonary Collateral Arteries (MAPCA)

Abstract

Ebstein's anomaly is a rare and complexed heart defect that affects the tricuspid valve and is accountable for around 1% of congenital cardiac abnormalities. It is one of the most common congenital causes of tricuspid valve regurgitation. Ebstein's anomaly is often diagnosed prenatally due to its severe cardiomegaly. Some individuals with this anomaly do not experience any complications until adulthood and even then its mostly minor complaints like exercise intolerance.  Atrial septal defect is most commonly (70-90%) associated with Ebstein's anomaly. However, ventricular septal defect (VSD) can be associated with 2-6% of the cases. This particular report presents a case of surgical intervention for a 20 years old female with Ebstein's anomaly that had multiple VSD's and a severe Pulmonary Stenosis (PS).

Author Biography

Prodip Kumar Biswas, MS, Department of Cardiac Surgery, National Heart Foundation Hospital & Research Institute, Dhaka, Bangladesh



References

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Published

2020-10-16

How to Cite

Das Gupta, S. ., Uddin, M., Howlader, S. S., Kumar Biswas, P. ., Kabiruzzaman, M., & Islam Talukder, M. Q. . (2020). Surgical management for an adult, female patient, with Ebstein Anomaly on Tricuspid Valve that has Subvalvular membrane with severe PS and multiple VSDs-A case report . The Heart Surgery Forum, 23(6), E781-E785. https://doi.org/10.1532/hsf.3233

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