Septum Primum Atrial Septal Defect in an Infant with Hypoplastic Left Heart Syndrome

Authors

  • Robert W. Loar
  • Harold M. Burkhart
  • Nathaniel W. Taggart

DOI:

https://doi.org/10.1532/HSF98.2014358

Abstract

Hypoplastic left heart syndrome (HLHS) is a form of congenital heart disease characterized by severe underdevelopment of the left heart, leading to inadequate systemic blood flow. Several different atrial septal morphologies are observed in HLHS, most commonly a secundum atrial septal defect, patent foramen ovale, intact septum, and leftward displacement of the superior attachment of the septum primum. It has been postulated that atrial septal development is associated with the development of the left heart. We present a case of a newborn infant with HLHS and the unusual finding of a primum ASD.

References

Lev M. 1952. Pathologic anatomy and interrelationship of hypoplasia of the aortic tract complexes. Lab Invest 1:61-70.nPark MV, Fedderly RT, Frommelt PC, et al. 2013. Leftward displacement of septum primum in hypoplastic left heart syndrome. Pediatr Cardiol 34:942-7.nTweddell JS, Hoffman GM, Mussatto KA, et al. 2002. Improved survival of patients undergoing palliation of hypoplastic left heart syndrome: lessons learned from 115 consecutive patients. Circulation 24:182-9.nWeinberg PM, Weindling S. 1988. Atrial septal anomalies differentiate types of hypoplastic left heart syndrome. J Am Coll Cardiol 12(suppl A):136A.nWilliams HJ, Tandon R, Edwards JE. 1974. Persistent ostium primum coexisting with mitral or tricuspid atresia. Chest 66:39-43.n

Published

2014-09-01

How to Cite

Loar, R. W., Burkhart, H. M., & Taggart, N. W. (2014). Septum Primum Atrial Septal Defect in an Infant with Hypoplastic Left Heart Syndrome. The Heart Surgery Forum, 17(4), E232-E233. https://doi.org/10.1532/HSF98.2014358

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