LVAD as a Bridge to Heart Transplantation in a Patient with Left Ventricular Noncompaction Cardiomyopathy and Advanced Heart Failure

Authors

  • Andraž Cerar Department of Cardiology, Advanced Heart Failure and Transplantation Center,University Medical Center, Ljubljana
  • JuÅ¡ KÅ¡ela Department of Cardiovascular Surgery, University Medical Center, Ljubljana
  • Gregor Poglajen Department of Cardiology, Advanced Heart Failure and Transplantation Center,University Medical Center, Ljubljana
  • Bojan Vrtovec Department of Cardiology, Advanced Heart Failure and Transplantation Center,University Medical Center, Ljubljana
  • Ivan Kneževič Department of Cardiovascular Surgery, University Medical Center, Ljubljana

DOI:

https://doi.org/10.1532/hsf.1563

Abstract

Left ventricular noncompaction cardiomyopathy (LVNC) is a rare hereditary cardiomyopathy characterized by the formation of an outer compacted and inner noncompacted layer of the myocardium. The latter is characterized by prominent trabeculations and deep intertrabecular recesses and is functionally inferior to the compacted myocardium. As there is no specific treatment for patients with LVNC who develop heart failure, the management of these patients is limited and many patients progress to advanced stages of the disease. For LVNC patients with advanced heart failure, the data regarding the use of mechanical circulatory support are scarce. We report a case of a 29-year-old patient with LVNC and advanced refractory heart failure, who was successfully bridged to heart transplantation using a long-term continuous-flow left ventricular assist device.

References

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Jenni R, Oechslin E, Schneider J, et al. 2001. Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction: a step towards classification as a distinct cardiomyopathy. Heart 86:666-71.

Paterick TE, Umland MM, Fuad Jan M, et al. 2012. Left ventricular noncompaction: A 25-Year Odyssey. J Am Soc Echocardiogr 24:363-75.

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Slaughter MS, Rogers JG, Milano CA, et al. 2009. Advanced heart failure treated with continuous-flow left ventricular assist device. N Engl J Med 361:2241-51.

Published

2016-06-24

How to Cite

Cerar, A., KÅ¡ela, J., Poglajen, G., Vrtovec, B., & Kneževič, I. (2016). LVAD as a Bridge to Heart Transplantation in a Patient with Left Ventricular Noncompaction Cardiomyopathy and Advanced Heart Failure. The Heart Surgery Forum, 19(3), E128-E130. https://doi.org/10.1532/hsf.1563

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Article