Recurrent Left Atrial Botyroid Rhabdomyosarcoma

  • Günseli Abay Department of Anesthesiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
  • Cemal Kocaaslan Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
  • Rafet Günay Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
  • Meryem Doğan Pathology Department, Haydarpasa Numune Hospital, Istanbul
  • Mahmut Murat Demirtaş Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul

Abstract

Primary heart tumors are extremely rare and their frequency ranges from approximately 0.01-0.3% in autopsy series. Nearly one quarter of all primary cardiac tumors are malignant tumors such as sarcoma. Rhabdomyosarcoma is the second most common malignant primary tumor of the heart following angiosarcoma.
Primary cardiac tumors present with one or more of the symptoms of the classic triad: cardiac symptoms and signs resulting from intracardiac obstruction; signs of systemic embolization; and systemic or constitutional symptoms. The prognosis after surgery is usually excellent in case of benign tumors, but is unfortunately still limited in localized malignant diseases [Butany 2005].
In this case report we present a 45-year-old female patient operated three times in 9 years because of left atrial tumor.

Author Biographies

Günseli Abay, Department of Anesthesiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
Anesthesiology Department
Cemal Kocaaslan, Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
Cardiovascular Surgery Department
Rafet Günay, Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
Cardiovascular Surgery Department
Meryem Doğan, Pathology Department, Haydarpasa Numune Hospital, Istanbul

Pathology Department

Mahmut Murat Demirtaş, Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul
Cardiovascular Surgery Department

References

Araoz PA, Eklund HE, Welsch TJ, Breen JF. 1999. CT and MR imaging of primary cardiac malignancies. Radiographics 19:1421-34.

Butany J, Nair V, Naseemuddin A, Nair GM, et al. 2005. Cardiac tumours: diagnosis and management. Lancet Oncology 4:219-28.

Chlumsky J, Hola D, Hlavacek K, et al. 2001. Cardiac rhabdomyosarcoma. Exp Clin Cardiol 6:114-17.

Karpuz V, İkitimur B, Karpuz H. 2007. A survey of heart tumors: clinical and echocardiographic approach. Anadolu Kardiyol Derg 7:427-35.

Steger CM, Hager T, Ruttmann E. 2012. Primary cardiac tumours: a single-center 41-year experience. ISRN Cardiol 2012: 906109.

Wexler LTT, Crist WM, Herman LJ. 2002. Rhabdomyosarcoma and the undifferentiated sarcomas. In: Pizzo PA, Poplack DG (eds), Principles and Practice of Pediatric Oncology. Philadelphia: Lippincott Williams & Wilkins, pp. 939-72.

Published
2016-05-09
How to Cite
Abay, G., Kocaaslan, C., Günay, R., Doğan, M., & Demirtaş, M. (2016). Recurrent Left Atrial Botyroid Rhabdomyosarcoma. The Heart Surgery Forum, 19(3), E097-E098. https://doi.org/10.1532/hsf.1418
Section
Articles