Successful One-Stage Operative Resection of an Intravenous Leiomyomatosis Involving the Right-Sided Heart Chambers and Pulmonary Artery
DOI:
https://doi.org/10.1532/hsf.1298Abstract
Intravenous leiomyomatosis (IVL) is a rare neoplastic disorder. It may extend into the right cardiac chambers, which are named after intracardiac leiomyomatosis (ICL). We describe a case of IVL extending into the right heart and pulmonary artery in a 46-year-old woman. The patient successfully underwent a one-stage operation under cardiopulmonary bypass (CPB) with deep hypothermic circulatory arrest. The patient fully recovered without major complications and did not exhibit any recurrence at the 9-month follow-up. The unique feature of this case is its involvement with the pulmonary artery, which is uncommon but potentially lethal.References
Birch-Hirschfeld FV. 1896. Lehrbuch der pathologischen anatomie, 5th ed. East Germany: FCW Vogel, Leipzig.
Durck H. 1907. Ueber ein kontinuierlich durch die untere Hohlvene in das Herz vorwachsendes Fibromyom des uterue. Muench Med Wochenschr 23:1154.
Gaudino M, Spatuzza P, Snider F, et al. 2002. Surgical management of a uterine leiomyoma extending through the inferior vena cava into the right heart. Heart Vessels 17:80-2.
Li B, Chen X, Chu YD, et al. 2013. Intracardiac leiomyomatosis: a comprehensive analysis of 194 cases. Interact Cardiovasc Thorac Surg 17:132-8.
Wang J, Yang J, Huang H, et al. 2012. Management of intracardiac leiomyomatosis with intracaval and intracardiac extension. Obstet Gynecol 120:1400-6.
Xu ZF, Yong F, Chen YY, et al. 2013. Uterine intravenous leiomyomatosis with cardiac extension: imaging characteristics and literature review. World J Clin Oncol 4:25-8.
Zhang CJ, Miao Q, Liu XR, et al. 2010. Intravenous leiomyomatosis with intracardiac extension. Ann Thorac Surg 89:1641-3.
