Scimitar Vein Anomaly with Total Right-Side Pulmonary Vein Return to Inferior Vena Cava Concomitant with Atresia of Upper Right-Side Pulmonary Vein and Secundum Atrial Septal Defect
DOI:
https://doi.org/10.1532/HSF98.20091017Abstract
Scimitar vein is the partial anomalous pulmonary venous connection usually draining lower pulmonary lobe to the inferior vena cava or right atrium. We present a scimitar vein anomaly in a 34-year-old woman with the uncommon association of a secundum type of atrial septal defect and atretic right upper pulmonary vein. She presented with increasing dyspenea for 2 months, however, she was asymptomatic in the past 10 years despite the presence of atrial septal defect. We describe its diagnostic and surgical approach.References
Brown J, Ruzmetov M, Minnich D, Vijay P, Edwards C, Uhlig P, et al. 2003. Surgical management of scimitar syndrome: An alternative approach. J Thorac Cardiovasc Surg 125:238-45.nCalhoun R, Mee R. 2003. A novel operative approach to scimitar syndrome. Ann Thorac Surg 76:301-3.nCasha A, Sulaiman M, Cale A. 2003. Repair of adult Scimitar syndrome with an intra-atrial conduit. Interact Cardiovasc Thorac Surg 2:128-30.nDupuis C, Charaf LA, Breviere GM, Abou P, Remy-Jardin M, Helmius G. 1992. The adult form of the Scimitar syndrome. Am J Cardiol 70:502-7.nDupuis C, Charaf LA, Breviere GM, Abou P. 1993. Infantile form of the Scimitar syndrome with pulmonary hypertension. Am J Cardiol 71:1326-30.nJuraszek A, Cohn H, van Praagh R, van Praagh S. 2005. Isolated left-sided scimitar vein connecting all left pulmonary veins to the right inferior vena cava. Pediatr Cardiol 26:846-7.nKamler M, Kerkhoff G, Budde T, Jakob H. 2003. Scimitar syndrome in an adult: diagnosis and surgical treatment. Interact Cardiovasc Thorac Surg 2:350-1.nKouchoukos NT, Black Stone EH, Doty DB, Hanley FL, Karp RB. 2003. Congenital heart disease: arterial septal and partial anomalous pulmonary venous connection. In: Kirklin JW, Barret-Boyes BG, editor. Cardiac Surgery. Philadelphia: ELSEVIER pp. 754.nLee M, Yang SH, Yang A. 2007. Transcatheter occlusion of the isolated scimitar vein anomaly camouflaged under dual pulmonary venous drainage of the right lung by the Amplatzer Ductal Occluder. Int J Cardiol 115:e90-e93.nRuggieri M, Abbate M, Parano E, Distefano A, Guarnera S, Pavone L. 2003. Scimitar Vein Anomaly With Multiple Cardiac Malformations, Craniofacial, and Central Nervous System Abnormalities in a Brother and Sister: Familial Scimitar Anomaly or New Syndrome? American Journal of Medical Genetics 116A:170-175.nWalles T, Lichtenberg A, Shiraga K, Kalima U. 2002. Combined correction of an adult Scimitar syndrome and coronary artery bypass grafting. Am Thorac Surg 73:640-2.n
