Right Ventricular Outflow Tract Myxoma with Absent Pulmonary Valve

Authors

  • Akira Yamaguchi, MD Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan
  • Hiroaki Sakamoto, MD, PhD Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan
  • Bryan J. Mathis, PhD Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan
  • Yutaka Watanabe, MD, PhD Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan
  • Hideyuki Kato, MD, PhD Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan
  • Yuji Hiramatsu, MD, PhD Department of Cardiovascular Surgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Japan

DOI:

https://doi.org/10.1532/hsf.4741

Keywords:

Myxoma, Absent pulmonary valve, right ventricular outflow tract

Abstract

Myxoma is the most common benign cardiac tumor. Absent pulmonary valves, often treated surgically in childhood, are associated with 3-6% of tetralogy of Fallot. It is unusual for absent pulmonary valves without other congenital heart diseases to be asymptomatic until adulthood. Here, we report the unique case of an 80-year-old female with right ventricular outflow tract myxoma and absent pulmonary valve that has, to our knowledge, never been reported. We successfully performed a simple mass resection and pulmonary valve implantation.

References

Allan LD, Sharland GK, Milburn A, et al. 1994. Prospective diagnosis of 1006 consecutive cases of congenital heart disease in the fetus. J Am Coll Cardiol. 23:1452–1458.

Gottschalk I, Jehle C, Herberg U, et al. 2017. Prenatal diagnosis of absent pulmonary valve syndrome from first trimester onward: novel insights into pathophysiology, associated conditions and outcome. Ultrasound Obstet Gynecol. 49:637–642.

Kasmeridis C, Katerinis E, Vogiatzis I. 2021. Asymptomatic, echocardiography-detected, right ventricular outflow tract sited myxoma. Anatol J Cardiol. 25:E32.

Mukadam ME, Kulkarni HL, Kumar CJ, Tendolkar AG. 1994. Right-ventricular myxoma presenting as right-ventricular outflow-tract obstruction--case report and review of the literature. Thorac Cardiovasc Surg. 42:243–6.

Pemberton J, Raudkivi P. 2012. Right ventricular myxoma causing pulmonary outflow tract obstruction. Interact Cardiovasc Thorac Surg. 14:362–3.

Reynen K. 1995. Cardiac myxomas. N Engl J Med 333:1610–7.

Sayger P, Lewis M, Arcilla R, Ilbawi M. 2000. Isolated congenital absence of a single pulmonary valve cusp. Pediatr Cardiol. 21:487-9.

Tanabe Y, Takahashi M, Kuwano H, et al. 1992. Long-term fate of isolated congenital absent pulmonary valve. Am Heart J 124:526–9.

Published

2022-06-22

How to Cite

Yamaguchi, A., Sakamoto, H., Mathis, B., Watanabe, Y., Kato, H., & Hiramatsu, Y. (2022). Right Ventricular Outflow Tract Myxoma with Absent Pulmonary Valve. The Heart Surgery Forum, 25(3), E459-E461. https://doi.org/10.1532/hsf.4741

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Section

Articles