Right Ventricular Outflow Tract Myxoma with Absent Pulmonary Valve
DOI:
https://doi.org/10.1532/hsf.4741Keywords:
Myxoma, Absent pulmonary valve, right ventricular outflow tractAbstract
Myxoma is the most common benign cardiac tumor. Absent pulmonary valves, often treated surgically in childhood, are associated with 3-6% of tetralogy of Fallot. It is unusual for absent pulmonary valves without other congenital heart diseases to be asymptomatic until adulthood. Here, we report the unique case of an 80-year-old female with right ventricular outflow tract myxoma and absent pulmonary valve that has, to our knowledge, never been reported. We successfully performed a simple mass resection and pulmonary valve implantation.
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