Damus-Kaye-Stansel Procedure with Extracardiac Fontan: Successful Recruitment of Previously Ligated Pulmonary Valve

Authors

  • Konrad Paczkowski Department of Pediatric Cardiac Surgery, Mikolaj Kopernik Hospital in Gdańsk
  • Ireneusz Haponiuk Department of Physiotherapy, Faculty of Rehabilitation and Kinesiology, Gdańsk University of Physical Education and Sport, Gdańsk
  • Maciej Chojnicki Department of Pediatric Cardiac Surgery, Mikolaj Kopernik Hospital in Gdańsk
  • Radosław Jaworski Department of Pediatric Cardiac Surgery, Mikolaj Kopernik Hospital in Gdańsk

DOI:

https://doi.org/10.1532/hsf.1580

Abstract

We present a case of a 2.5-year-old-girl with complex congenital heart disease: tricuspid atresia (TA), bulboventricular septal defect (VSD), hypoplastic right ventricle, d-transposition
of the great arteries (d-TGA) with aortic outflow from redundant RV. Due to II/III degree atrioventricular block induced after diagnostic cardiac catheterization, an epicardial pacemaker was implanted during the Glenn procedure. Because of severe left ventricle outflow tract obstruction, she was finally referred for extracardiac TCPC (extracardiac Fontan type) with recruitment of PV and Damus-Kaye-Stansel anastomosis. Intraoperatively, the pulmonary trunk stump was opened and a competent pulmonary valve with flaccid leaflets was found. Simple ligation of the pulmonary trunk with a preserved pulmonary valve enabled an effective aorto-pulmonary bridging of systemic outflow tract with the use of natural fully competent ventricle-arterial valves. The relief of single ventricle outflow tract obstruction led to final stabilization of spontaneous sinus rhythm recovery after
2 years of pacemaker stimulation.

References

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Published

2016-08-23

How to Cite

Paczkowski, K., Haponiuk, I., Chojnicki, M., & Jaworski, R. (2016). Damus-Kaye-Stansel Procedure with Extracardiac Fontan: Successful Recruitment of Previously Ligated Pulmonary Valve. The Heart Surgery Forum, 19(4), E206-E207. https://doi.org/10.1532/hsf.1580

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