Multidetector Computed Tomography Findings of Ectopia Cordis and Other Components of Pentalogy of Cantrell: A Case Report
DOI:
https://doi.org/10.1532/HSF98.20061135Abstract
We report a case of ectopia cordis assessed with multidetector computed tomography (MDCT). Accurate and early diagnosis in components of pentalogy of Cantrell is vital for surgical planning and assessment of prognostic factors. Postnatal MDCT imaging allows for optimal assessment of the fetus with ectopia cordis, which has significant implications in terms of preoperative planning and obtaining prognostic information.References
Cantrell JR, Haller JA, Ravitch MM. 1958. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium and heart. Surg Gynecol Obstet 107:602-14.nCarmi R, Boughman JA. 1992. Pentalogy of Cantrell and associated midline anomalies: a possible ventral midline developmental field. Am J Med Genet 42:90-5.nDi Bernardo S, Sekarski N, Meijboom E. 2004. Left ventricular diverticulum in a neonate with Cantrell syndrome. Heart 90:1320.nMartin RA, Cunniff C, Erickson L, Jones KL. 1992. Pentalogy of Cantrell and ectopia cordis, a familial developmental field complex. Am J Med Genet 42:839-41.nMorales JM, Patel SG, Duff JA, Villareal RL, Simpson JW. 2000. Ectopia cordis and other midline defects. Ann Thorac Surg 70:111-114.nVazquez-Jimenez JF, Eberhard GM, Muehler EG, Daebritz S, et al. 1998. Cantrell's syndrome: a challenge to the surgeon. Ann Thorac Surg 65:1178-85.nGhidini A, Sirtori M, Romero R, Hobbins JC. 1998. Prenatal diagnosis of pentalogy of Cantrell. J Ultrasound Med 7:567-72.nHalbertsma FJ, van Oort A, van der Staak F. 2002. Cardiac diverticulum and omphalocele: Cantrell's pentalogy or syndrome. Cardiol Young 12:71-4.nHaynor DR, Shuman WP, Brewer DK, Mack LA. 1984. Imaging of fetal ectopia cordis: roles of sonography and computerized tomography. J Ultrasound Med 3:25-7.nHornberger LK, Colan SD, Lock JE, Wessel DC, Mayer J et al. 1996. Outcome of patients with ectopia cordis and significant intra-cardiac defects. Circulation 94(9 Suppl)II32-7.n
