Primary Cardiac Rhabdomyosarcoma of the Right Atrium: Case Report
DOI:
https://doi.org/10.1532/HSF98.20071176Abstract
Rhabdomyosarcoma is a rare malignant tumor of the heart that accounts for 20% of all primary malignant neoplasms of the heart. Symptoms vary in accordance with the location of the mass; unfortunately, by the time the patient becomes symptomatic, the tumor has already metastasized to other organs. Diagnosis is frequently obtained via transthoracic or transesophageal echocardiography and nuclear magnetic resonance imaging. Surgery is indicated for malignant cardiac neoplasms to relieve cardiac symptoms and to prolong patient survival. Subsequent postoperative chemotherapy or radiotherapy is necessary, and the long-term prognosis is poor. We present a case of a primary cardiac rhabdomyosarcoma that arose from the lateral wall of the right atrium and required implantation of a permanent cardiac pacemaker after surgery.References
Castorino F, Masiello P, Quattrocchi E, Di Benedetto G. 2000. Primary cardiac rhabdomyosarcoma of the left atrium. Tex Heart Inst J 27:206-8.nCentofanty P, Di Rosa E, Deorsola L, et al. 1999. Primary cardiac tumors: early and late results of surgical treatment in 91 patients. Ann Thorac Surg 68:1236-41.nChan HS, Sonley MJ, Moes CA, Daneman A, Smith CR, Martin DJ. 1985. Primary and secondary tumors of childhood involving the pericardium and great vessels: a report of 75 cases and review of the literature. Cancer 56:825-36.nChitwood WR Jr. 1988. Cardiac neoplasms: current diagnosis, pathology, and therapy. J Card Surg 3:119-54.nHolley DG, Martin GR, Brenner JI, et al. 1995. Diagnosis and management of fetal cardiac tumors: a multicenter experience and review of published reports. J Am Coll Cardiol 26:516-20.nMcFadden PM, Ochsner JL. 1997. Atrial replacement and tricuspid valve reconstruction after angiosarcoma resection. Ann Thorac Surg 64:1164-7.nMurphy MC, Sweeney MS, Putnam JB Jr, et al. 1990. Surgical treatment of cardiac tumors: a 25-year experience. Ann Thorac Surg 49:612-8.nReeder GS, Khandheria BK, Seward JB, Tjik AJ. 1991. Transesophageal echocardiography and cardiac masses. Mayo Clin Proc 66:1101-9.nSchmaltz AA, ApitzJ. 1981. Primary heart tumors in infancy and childhood: report of four cases and review of literature. Cardiology 67:12-22.n
